Email: moc. Received Sep 30; Accepted Oct Copyright Quantitative Imaging in Medicine and Surgery. All rights reserved. This article has been cited by other articles in PMC.
|Published (Last):||12 February 2005|
|PDF File Size:||4.41 Mb|
|ePub File Size:||19.10 Mb|
|Price:||Free* [*Free Regsitration Required]|
Manas R. E-mail: ni. This article has been cited by other articles in PMC. Abstract A month-old male child presented with recurrent generalized seizures, spastic hemiplegia, microcephaly and had developmental delay in motor and speech domains.
CT of the brain revealed characteristic features diagnostic of infantile type of cerebral hemiatrophy or Dyke-Davidoff-Masson syndrome. Keywords: Dyke-Davidoff-Masson syndrome, hemiatrophy Introduction Dyke-Davidoff-Masson syndrome DDMS refers to atrophy or hypoplasia of one cerebral hemisphere hemiatrophy , which is usually due to an insult to the developing brain in fetal or early childhood period.
More commonly they present with recurrent seizures, facial asymmetry, contralateral hemiplegia, mental retardation or learning disability, and speech and language disorders. Sensory loss and psychiatric manifestations like schizophrenia had been reported rarely. The syndrome had been documented mainly in adolescents and adults. Case Report A month-old male child, born full term, to non-consanguineous parents, presented with recurrent generalized seizures for last 4 months.
There was no history of significant antenatal or perinatal complications. He had delayed milestones of development in the form of not able to stand or walk and not spoken a word. The bilateral carotid pulsations were normal with no bruit. Vision and hearing were normal, and cranial nerves were intact.
Neurological examination revealed right-sided spastic hemiparesis with brisk tendon reflexes and extensor planter response, other systemic examinations being normal. A plain and contrast CT of the brain was done which revealed atrophy of left cerebral hemisphere with dilatation of the ipsilateral ventricle, widening of sulci and sylvian fissure on the same side.
There was also shift of midline to left and thickening of calvarium on the left side [ Figure 1 ]. He responded well to the drug followed by sessions of physiotherapy. He was seizure free for next 3 months but then unfortunately lost for follow-up.
Abstract Background Dyke-Davidoff-Masson syndrome is a rare condition of unknown frequency resulting from brain injury due to a multitude of causes; especially in early life. Case presentation We present a case of a year-old girl who initially presented with headaches, followed by episodic complex-partial seizures; which was controlled via medication. She also had right sided hemiparesis. Computed tomography CT showed evidence of left parieto-temporal infarct with cerebral atrophy. Complementary magnetic resonance imaging MRI did not reveal additional information.
Dyke-Davidoff-Masson syndrome: a case report
Dyke-Davidoff-Masson syndrome: imaging features with illustration of two cases